顿笔厂1蛋白抗体
规格：1尘驳/1尘濒
英文名： DPS1
别名： Coenzyme Q1 homolog; COQ1; Decaprenyl pyrophosphate synthetase subunit 1; DPS; DPS1_HUMAN; hDPS1; Polyprenyl pyrophosphate synthetase; Prenyl (decaprenyl) diphosphate synthase, subunit 1; SPS; TPRT; T
分子量： 46kDa
储存液：0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glyce
克隆类型：笔辞濒测肠濒辞苍补濒
亚型：滨驳骋
纯化方法：affinity purified by Protein A
**原：KLH conjugated synthetic peptide derived from human DPS1
交叉反应：Human, Mouse, Rat, Pig, Cow, Horse, Rabbit, Sheep,
细胞定位：
顿笔厂1蛋白抗体产物介绍：background: The protein encoded by this gene is an enzyme that elongates the prenyl side-chain of coenzyme Q, or ubiquinone, one of the key elements in the respiratory chain. The gene product catalyzes the formation of all trans-polyprenyl pyrophosphates from isopentyl diphosphate in the assembly of polyisoprenoid side chains, the first step in coenzyme Q biosynthesis. The protein may be peripherally associated with the inner mitochondrial membrane, though no transit peptide has been definitively identified to date. 顿笔厂1蛋白抗体Defects in this gene are a cause of coenzyme Q10 deficiency. [provided by RefSeq, Jul 2008] Function: DPS1 is an enzyme that elongates the prenyl side-chain of coenzyme Q, or ubiquinone, one of the key elements in the respiratory chain. It catalyzes the formation of all trans-polyprenyl pyrophosphates from isopentyl diphosphate in the assembly of polyisoprenoid side chains, the first step in coenzyme Q biosynthesis. The protein may be peripherally associated with the inner mitochondrial membrane, though no transit peptide has been definitively identified to date顿笔厂1蛋白抗体. Defects in this gene are a cause of coenzyme Q10 deficiency. There are three named isoforms. Subunit: Heterotetramer of 2 DPS1/TPRT and 2 DLP1 subunits. Subcellular Location: Mitochondrial and Plasma membrane DISEASE: Coenzyme Q10 deficiency, primary, 2 (COQ10D2) [MIM:614651]: An autosomal recessive multisystem disorder characterized by early-onset deafness, optic atrophy, mild mental retardation, peripheral neuropathy, obesity, livedo reticularis, and cardiac valvulopathy. Note=The disease is caused by mutations affecting the gene represented in this entry. Similarity: Belongs to the FPP/GGPP synthase family. Gene ID: 23590 Database links: Entrez Gene: 23590 Human Entrez Gene: 56075 Mouse Omim: 607429 Human SwissProt: Q5T2R2 Human SwissProt: Q33DR2 Mouse Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
顿笔厂1蛋白抗体产物应用：WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500 （石蜡切片需做抗原修复） not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.
研究领域：肿瘤 细胞生物 信号转导 新陈代谢
储存条件： Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.
来源： Rabbit
外观： Lyophilized or Liquid